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Table 5 Assessment of coverage of HAE attack warning signs by the HAE PRO

From: Development and content validity testing of a patient-reported outcomes questionnaire for the assessment of hereditary angioedema in observational studies

Warning signs assessed by HAE PRO and mentioned by patients

Additional warning signs mentioned by patients (n = 43)

Skin redness (n = 13)

Pain (n = 4)

Irritability (n = 11)

Itchiness (n = 4)

Nausea (n = 8)

Burning (n = 4)

Skin sensation (n = 7)

None (n = 4)

Tiredness (n = 7)

Feeling of butterflies (n = 3)

Skin Tightness (n = 6)

Swelling (n = 3)

Aggressiveness (n = 3)

Red rings on the skin (n = 3)

Sensitivity to noise (n = 3)

Stress (n = 2)

Hunger (n = 2)

Headaches (n = 2)

Prickling (n = 1)

Thirst (n = 2)

 

Difficulty breathing (n = 2)

 

Numbness (n = 2)