Age (years) | 57 | ± | 16 |
---|---|---|---|
Male, n (%) | 8 (27) | ||
BMI (kg/m2) | 23.3 | ± | 4.8 |
WHO functional classification II/III/IV | 5/15/10 | ||
Idiopathic/porto/CTD | 13/6/11 | ||
Laboratory | |||
 BNP (pg/mL) * | 391 (69–558) | ||
Swan–Ganz data | |||
 RAP (mm Hg) | 6.1 | ± | 4.2 |
 Systolic PAP (mm Hg) | 73.9 | ± | 20.2 |
 Diastolic PAP (mm Hg) | 28.9 | ± | 8.5 |
 Mean PAP (mm Hg) | 46 | ± | 12 |
 PAWP (mm Hg) | 9 | ± | 4.3 |
 CO (L/min) | 4.06 | ± | 1.42 |
 CI (L/min/m2) | 2.68 | ± | 0.93 |
 PVR (Wood units) | 11.3 | ± | 6.8 |
 SvO2 (%) | 64.1 | ± | 8.9 |
Pulmonary Function Testing | |||
 FEV1% | 76.9 | ± | 11.2 |
 %VC | 87.4 | ± | 19.8 |
 %DLCO | 61.2 | ± | 26.4 |
Cardiopulmonary Exercise Testing | |||
 Peak VO2 (mL/min/kg) | 12.1 | ± | 4.4 |
 VE/VCO2 slope | 55.1 | ± | 20.3 |