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Table 2 Peds QoL Generic and Fatigue Scores: In relation to norms

From: Health-related quality of life in children with congenital adrenal hyperplasia

QoL Score, Mean

Children with CAH

Healthy Children

Mean difference (95% CI)

Parents, CAH Children

Parents, Healthy Children

Mean difference (95% CI)

Generic QoL Scores (Overall and subscales)

 Overall

82.71 (n = 32)

83.00 (n = 401)

−0.29 (−.25, 5.67)

83.90 (n = 43)

87.61 (n = 717)

−3.71 (−7.37, −0.05)a

 Physical

90.53 (n = 32)

84.41 (n = 400)

6.12 (2.10, 10.14)a

89.10 (n = 44)

89.32 (n = 717)

−0.22 (−3.52, 3.08)

 Emotional

80.16 (n = 32)

80.86 (n = 400)

−0.70 (−6.96, 5.55)

75.90 (n = 44)

82.64 (n = 717)

−6.74 (−12.36, −1.12)a

 Social

85.16 (n = 32)

87.42 (n = 399)

−2.26 (−10.11, 5.58)

90.60 (n = 43)

91.56 (n = 716)

−0.96 (−4.57, 2.65)

 School

75.00 (n = 32)

78.63 (n = 386)

−3.63 (−9.78, 2.52)

78.99 (n = 40)

85.47 (n = 611)

−6.48 (−12.75, −0.21)a

Fatigue Scores (Overall and subscales)

 Overall

79.08 (n = 32)

80.49 (n = 52)

−1.41 (−7.85, 5.02)

81.90 (n = 42)

89.63 (n = 102)

−7.73 (−12.24, −3.22)a

 General

82.81 (n = 32)

85.34 (n = 52)

−2.53 (−9.13, 4.07)

82.40 (n = 42)

89.30 (n = 102)

−6.90 (−12.34, −1.46)a

 Sleep/Rest

74.48 (n = 32)

75.00 (n = 52)

−0.52 (−8.30, 7.25)

81.60 (n = 42)

88.86 (n = 102)

−7.26 (−12.14, −2.38)a

 Cognitive

79.97 (n = 31)

81.14 (n = 52)

−1.17 (−10.71, 8.37)

81.60 (n = 42)

90.72 (n = 102)

−9.12 (−15.72, −2.52)a

  1. aIndicates a significant finding at the 0.05 significance level
  2. CAH congenital adrenal hyperplasia, QoL quality of life