Fig. 1From: Structural equation modeling of the quality of life for patients with marfan syndromeResearch framework. FH of MFS = family history of Marfan syndrome; Ao = sinus of Valsalva of diameter Z (= Z score), indicating the presence of aortic root dilatation (when standardized with respect to age and body size); FEN 1 = fibrillin-1 mutation; EL = ectopia lentis; OP of CV = operation on the cardiovascular systemBack to article page